Argininemia.

Deficiency of Arginase damage to ARG 1 gene.
Progressive spastic diplegia
Scissoring of lower extremities
Choreo athetotic movements.
Loss of developmental milestones in a Normal infant.

Least Hyperammonemia.
Urine contains: COLA - Cysteine,ornithine,lysine, Arginine.
Alpha ketoguanidinovaleric acid